1例完全型Shone综合征合并重度肺动脉高压患儿的康复护理

doi:10.3761/j.issn.0254-1769.2026.08.014

中华护理杂志 ›› 2026, Vol. 61 ›› Issue (8): 1107-1111.DOI: 10.3761/j.issn.0254-1769.2026.08.014

1例完全型Shone综合征合并重度肺动脉高压患儿的康复护理

刘素玲(), 蒋伟红, 李晓艳, 唐晓敏^*()

浙江大学医学院附属儿童医院心脏外科杭州市 310052

收稿日期:2025-08-07 出版日期:2026-04-20 发布日期:2026-04-22
*通讯作者: 唐晓敏，E-mail：xiaomintang@zju.edu.cn
作者简介:刘素玲：女，本科，护师，E-mail：2466129026@qq.com
第一联系人：作者贡献声明
刘素玲：选题设计、资料收集及论文撰写；蒋伟红、李晓艳：文献检索；唐晓敏：论文审阅和修改
基金资助:
浙江省医药卫生科技计划一般项目(2025KY935)

Rehabilitation nursing care for a child with complete Shone’s syndrome and severe pulmonary hypertension

LIU Suling(), JIANG Weihong, LI Xiaoyan, TANG Xiaomin^*()

Department of Cardiac Surgery， Children’s Hospital，Zhejiang University School of Medicine， Hangzhou 310052， China.

Received:2025-08-07 Online:2026-04-20 Published:2026-04-22
* Corresponding author: TANG Xiaomin，E-mail：xiaomintang@zju.edu.cn
Funding program:
General Program of Zhejiang Provincial Medical and Health Science and Technology Plan(2025KY935)

摘要/Abstract

摘要：

总结1例完全型Shone综合征合并重度肺动脉高压患儿的康复护理经验。护理要点：实施预康复护理，优化术前生理状态；强化肺动脉高压管理，预防全心衰竭；维持循环系统稳定，降低恶性心律失常的发生风险；提供序贯式呼吸功能支持，促进肺功能恢复；实施阶梯式营养支持，改善营养状况；做好随访监测与指导，提升延续性护理质量。经过17 d精心的治疗与护理，患儿顺利出院，随访2个月，心脏超声提示心脏瓣膜及功能良好，二尖瓣少量反流，未见残余梗阻。

关键词: Shone综合征, 重度肺动脉高压, 康复护理, 儿科护理学

Abstract:

To summarize the nursing experience regarding the rehabilitation of a child with complete Shone’s syndrome complicated by severe pulmonary hypertension. Key nursing interventions included：implementing pre-rehabilitation to optimize preoperative physiological status；reinforcing the management of pulmonary hypertension associated with left heart disease to prevent global heart failure；maintaining hemodynamic stability to reduce the risk of malignant arrhythmias；providing sequential respiratory support to promote pulmonary function recovery；implementing stepwise nutritional support to improve nutritional status；conducting follow-up monitoring and guidance to enhance the quality of continuity of care. After 17 days of meticulous treatment and nursing，the child was discharged successfully. At the 2-month follow-up，cardiac ultrasound indicated favorable cardiac valve and heart function，with only mild mitral regurgitation and no residual obstruction observed.

Key words: Shone’s Syndrome, Severe Pulmonary Hypertension, Rehabilitation Nursing, Pediatric Nursing

刘素玲, 蒋伟红, 李晓艳, 唐晓敏. 1例完全型Shone综合征合并重度肺动脉高压患儿的康复护理[J]. 中华护理杂志, 2026, 61(8): 1107-1111.

LIU Suling, JIANG Weihong, LI Xiaoyan, TANG Xiaomin. Rehabilitation nursing care for a child with complete Shone’s syndrome and severe pulmonary hypertension[J]. Chinese Journal of Nursing, 2026, 61(8): 1107-1111.

参考文献 15

[1]	True A, Baidya M, Lui C, et al. Computed tomography imaging characteristics of shone syndrome[J]. Radiol Case Rep, 2018, 14(2):164-167. DOI URL
[2]	Zhao QM, Liu F, Wu L, et al. Prevalence of congenital heart disease at live birth in China[J]. J Pediatr, 2019, 204:53-58. DOI URL
[3]	Elmahrouk AF, Ismail MF, Arafat AA, et al. Outcomes of biven-tricular repair for shone’s complex[J]. J Card Surg, 2021, 36(1):12-20. DOI PMID
[4]	国家心血管病中心肺动脉高压专科联盟, 国家心血管病专家委员会右心与肺血管病专业委员会. 中国肺动脉高压诊治临床路径[J]. 中国循环杂志, 2023, 38(7):691-703.
	China Specialty Alliance for Pulmonary Hypertension,National Center for Cardiovascular Diseases; National Committee of Right Heart and Pulmonary Vascular Diseases of National Expert Commission for Care. Chinese clinical pathway for diag-nosis and treatment of pulmonary hypertension[J]. Chin Circ J, 2023, 38(7):691-703.
[5]	曹跃丰, 李磊, 苏俊武, 等. 儿童Shone综合征22例疾病特点与手术效果分析[J]. 中华实用儿科临床杂志, 2022, 37(6):443-445.
	Cao YF, Li L, Su JW, et al. Analysis of disease characteristics and surgical effect of 22 cases of Shone syndrome in children[J]. Chin J Appl Clin Pediatr, 2022, 37(6):443-445.
[6]	中华医学会儿科学分会心血管学组, 中国医师协会心血管内科医师分会儿童心血管专业委员会, 中华儿科杂志编辑委员会, 等. 儿童心力衰竭诊断和治疗建议(2020年修订版)[J]. 中华儿科杂志, 2021, 59(2):84-94.
	Cardiovascular Group of the Pediatrics Branch of the Chinese Medical Association, Pediatric Cardiovascular Professional Com-mittee of the Cardiovascular Physicians Branch of the Chinese Medical Doctor Association, Editorial Committee of the Chinese Journal of Pediatrics, et al. Recommendations for diagnosis and treatment of heart failure in children(2020 revised edition)[J]. Chin J Pediatr, 2021, 59(2):84-94.
[7]	潘婷, 卢山, 苏云艳, 等. 心脏外科患者围手术期营养管理的最佳证据总结[J]. 中华现代护理杂志, 2025, 31(13):1721-1730.
	Pan T, Lu S, Su YY, et al. Summary of best evidence for pe-rioperative nutrition management in cardiac surgery patients[J]. Chin J Mod Nurs, 2025, 31(13):1721-1730.
[8]	刘亚飞, 邢海英, 莫粤, 等. 1例Uhl’s畸形患儿行复杂心脏手术的术后护理[J]. 中华护理杂志, 2025, 60(10):1261-1265. DOI URL
	Liu YF, Xing HY, Mo Y, et al. The postoperative nursing care of a child with Uhl’s anomaly undergoing complex heart surgery[J]. Chin J Nurs, 2025, 60(10):1261-1265. DOI URL
[9]	黄盼盼, 李丽玲, 胡晓静. 先天性心脏病婴儿早期运动康复的研究进展[J]. 中华护理杂志, 2025, 60(9):1050-1055. DOI URL
	Huang PP, Li LL, Hu XJ. Research progress of early exercise rehabilitation in infants with congenital heart disease[J]. Chin J Nurs, 2025, 60(9):1050-1055. DOI URL
[10]	申晓敏, 贺文静, 杨同男, 等. Ⅱ型Abernethy畸形合并肺动脉高压患者行肝移植的术后护理[J]. 中华急危重症护理杂志, 2025, 6(5):579-581. DOI
	Shen XM, He WJ, Yang TN, et al. Postoperative nursing of a patient with type Ⅱ Abernethy malformation complicated with pulmonary hypertension undergoing liver transplantation[J]. Chin J Emerg Crit Care Nurs, 2025, 6(5):579-581.
[11]	邵珍珍, 朱琳, 唐文娟, 等. 儿童术后疼痛评估工具研究进展[J]. 护理学杂志, 2021, 36(5):102-108.
	Shao ZZ, Zhu L, Tang WJ, et al. A review on postoperative pain assessment tools in children[J]. J Nurs Sci, 2021, 36(5):102-108.
[12]	王丹瑾, 张明杰, 宋奕霄, 等. 儿童Fontan术后心律失常[J]. 中国小儿急救医学, 2025, 32(7):519-523.
	Wang DJ, Zhang MJ, Song YX, et al. Arrhythmia after Fontan surgery in children[J]. Pediat Em Med, 2025, 32(7):519-523.
[13]	戎丹青, 卫建华, 翁峰霞, 等. 1例重度肺动脉高压合并巨大心脏患者行双肺移植的术后护理[J]. 中华护理杂志, 2025, 60(8):977-981. DOI URL
	Rong DQ, Wei JH, Weng FX, et al. Nursing care of a patient with severe pulmonary hypertension combined with giant heart after double lung transplantation[J]. Chin J Nurs, 2025, 60(8):977-981. DOI URL
[14]	黄坚鹄, 张悦玥, 王伟, 等. 营养支持在先天性心脏病术后ECMO辅助中的差异分析[J]. 中华小儿外科杂志, 2024, 45(9):802-805.
	Huang JH, Zhang YY, Wang W, et al. Nutritional support differences in postoperative ECMO assistance for congenital heart disease[J]. Chin J Pediatr Surg, 2024, 45(9):802-805.
[15]	Perrier SL, Jadhav M, d’Udekem Y, et al. Multiple left-sided stenotic lesions:outcomes after mitral valve surgery. Arguments for abandoning the eponym ‘shone syndrome’[J]. Eur J Car-diothorac Surg, 2020, 58(3):567-573.

1例完全型Shone综合征合并重度肺动脉高压患儿的康复护理

Rehabilitation nursing care for a child with complete Shone’s syndrome and severe pulmonary hypertension

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