doi:10.3761/j.issn.0254-1769.2020.06.026

Abstract

Key words: Hereditary Diffuse Leukoencephalopathy with Spheroids, Hematopoietic Stem Cell Transplantation, Nursing Care

摘要：

对1例无法行走,认知功能低下,大小便失禁,抑郁状态又易激惹的遗传性弥漫性白质脑病合并轴索球样变患者进行异基因造血干细胞移植,护理要点包括：对陪护家属进行医院感染相关知识和技能的培训及考核;化疗期间提前使用止吐药物干预,饮食上添加增稠剂并联合呼吸肌训练来减少患者呛咳及误吸的发生;进行四肢主动及被动运动,维持患者肌肉功能状态;不断变换思路来应对患者排便失禁;易激惹患者及照护者的心理护理;移植后密切监测感染、出血倾向及移植物抗宿主病等并发症。经过精心的治疗及护理,造血干细胞成功植入,入无菌仓26 d后患者转至普通病房继续治疗。

关键词: 遗传性弥漫性白质脑病合并轴索球样变, 造血干细胞移植, 护理

周晓瑜, 黄丽华, 金爱云, 章建丽, 缪娟, 许丽炜. 1例遗传性弥漫性白质脑病合并轴索球样变患者行造血干细胞移植的护理[J]. 中华护理杂志, 2020, 55(6): 928-931.

References 14

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1例遗传性弥漫性白质脑病合并轴索球样变患者行造血干细胞移植的护理

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