Perioperative nursing care of a patient with glycogen storage disease type Ⅲa under-going living donor liver transplantation

doi:10.3761/j.issn.0254-1769.2025.21.003

Abstract

Abstract:

This report summarizes the perioperative nursing care of a patient with glycogen storage disease（GSD） type Ⅲa who underwent living donor liver transplantation. Key nursing strategies included：enhanced nutritional support and blood glucose control to maintain metabolic stability before surgery；comprehensive preoperative assessment of myocardial and skeletal muscle function with multidimensional fall prevention measures. Postoperatively，multi-dimensional precise monitoring and management were implemented to support graft function recovery. A stepwise nutritional intervention was adopted to sustain glucose homeostasis and meet diverse nutritional needs. Cardiac function-guided rehabilitation planning enabled individualized phased rehabilitation training. A comprehensive health record was established to ensure continuity of care through structured and continuous follow-up. The patient recovered well and was discharged without complications. At 3-month follow-up，the recovery remained satisfactory.

Key words: Liver Transplantation, Glycogen Storage Disease, Liver Cirrhosis, Perioperative Nursing

摘要：

总结1例糖原累积综合征Ⅲa型患者行活体肝脏移植的围手术期护理经验。护理要点如下：强化营养支持与血糖调控，维持术前代谢稳定；评估心肌及骨骼肌功能，多维度预防跌倒；术后开展多维度精准监测调控，促进移植肝脏功能重建；进行阶梯式营养支持，维持糖代谢稳态，满足多元营养需求；开展以心功能为核心的综合评估，实施个性化分阶段康复训练；建立全程健康档案，落实随访管理。患者术后顺利出院，出院后随访3个月，恢复良好。

关键词: 肝移植, 糖原累积综合征, 肝硬化, 围手术期护理

SU Qian, LI Yue, CHEN Hongshuang, PAN Xinwei, FENG Lujing, WU Yu, XU Xuelei. Perioperative nursing care of a patient with glycogen storage disease type Ⅲa under-going living donor liver transplantation[J]. Chinese Journal of Nursing, 2025, 60(21): 2579-2583.

苏倩, 李越, 陈红爽, 潘新伟, 冯璐晶, 吴宇, 徐雪蕾. 1例糖原累积综合征Ⅲa型患者行活体肝脏移植的围手术期护理[J]. 中华护理杂志, 2025, 60(21): 2579-2583.

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