Abstract:

This paper summarizes the nursing experience of liver transplantation for a patient with postpartum delayed ornithine transcarbamylase deficiency complicated with hyperammonemia encephalopathy. The key points of preoperative care include initiating a multidisciplinary treatment team and providing meticulous care management throughout the entire process；implementing proactive care to prevent blood clots in the tubing；monitoring the changes in the condition in real time and maintaining the stable state of the body；dynamically adjusting the nutritional plan to enhance patients’ tolerance to surgery. The key points of postoperative care include closely monitoring the function of the transplanted liver and preventing the occurrence of rejection reactions；implementing a systematic and comprehensive management plan to reduce postoperative complications；strengthening the long-term follow-up management of patients and dynamically tracking their health. After meticulous treatment and care，the patient was discharged from the hospital after 39 days of hospitalization. The patient was followed up for 2 months and was in good condition.

Key words: Ornithine Transcarbamylase Deficiency, Hyperammonemia Encephalopathy, Liver Transplantation, Perioperative Care

摘要：

总结1例产后迟发型鸟氨酸氨甲酰转移酶缺乏症合并高血氨脑病患者行肝移植的护理经验。术前护理要点包括启动多学科治疗团队，提供全程精细化照护管理；实施预见性护理，防止管路凝血；实时监测病情变化，维持机体稳定状态；动态调整营养方案，提升患者手术耐受度。术后护理要点包括密切监测移植肝功能，防范排斥反应的发生；落实系统化综合管理，降低术后并发症；做好长期随访管理，动态追踪患者健康。经过精心的治疗和护理，患者住院39 d后康复出院。随访2个月，患者状况良好。

关键词: 鸟氨酸氨甲酰转移酶缺乏症, 高血氨脑病, 肝移植, 围手术期护理