Nursing care of a child with hepatolenticular degeneration complicated with renal failure undergoing liver transplantation

doi:10.3761/j.issn.0254-1769.2022.02.014

Abstract

Abstract:

To summarize the nursing experience of a child with hepatolenticular degeneration complicated by renal failure undergoing liver transplantation. The main points of nursing include strict monitoring of kidney function,good anticoagulation management,timely adjustment of treatment plans,personalized rehabilitation and diet guidance,strict implementation of disinfection and isolation measures throughout the process,close monitoring of transplanted liver function,and provision of a hospital-family-social support system. After careful treatment and care,the child was discharged on foot 55 days after the operation. The patient was followed up for 6 months and recovered well.

Key words: Hepatolenticular Degeneration, Renal Failure, Liver Transplantation, Pediatric Nursing

摘要：

总结1例肝豆状核变性并发肾功能衰竭患儿行肝移植术的护理经验。护理要点：严密监测肾功能,加强抗凝管理,及时调整治疗方案;开展个性化的康复及饮食指导;动态监测移植肝功能,严格落实消毒隔离措施,预防感染和排斥反应;构建医院-家庭-社会支持系统。经过精心的治疗及护理,患儿术后55 d步行出院,随访6个月,恢复良好。

关键词: 肝豆状核变性, 肾功能衰竭, 肝移植, 儿科护理学

LU Lu, LU Fangyan, ZHANG Wanying, YAO Caiping. Nursing care of a child with hepatolenticular degeneration complicated with renal failure undergoing liver transplantation[J]. Chinese Journal of Nursing, 2022, 57(2): 208-211.

卢露, 卢芳燕, 张婉莹, 姚彩萍. 1例肝豆状核变性并发肾功能衰竭患儿行肝移植术的护理[J]. 中华护理杂志, 2022, 57(2): 208-211.

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