关键词: 鸟氨酸氨甲酰转移酶缺乏症, 高血氨脑病, 肝移植, 围手术期护理

Abstract:

This paper summarizes the nursing experience of liver transplantation for a patient with postpartum delayed ornithine transcarbamylase deficiency complicated with hyperammonemia encephalopathy. The key points of preoperative care include initiating a multidisciplinary treatment team and providing meticulous care management throughout the entire process；implementing proactive care to prevent blood clots in the tubing；monitoring the changes in the condition in real time and maintaining the stable state of the body；dynamically adjusting the nutritional plan to enhance patients’ tolerance to surgery. The key points of postoperative care include closely monitoring the function of the transplanted liver and preventing the occurrence of rejection reactions；implementing a systematic and comprehensive management plan to reduce postoperative complications；strengthening the long-term follow-up management of patients and dynamically tracking their health. After meticulous treatment and care，the patient was discharged from the hospital after 39 days of hospitalization. The patient was followed up for 2 months and was in good condition.

Key words: Ornithine Transcarbamylase Deficiency, Hyperammonemia Encephalopathy, Liver Transplantation, Perioperative Care