关键词: 肺泡蛋白沉积症, 支气管肺泡灌洗, 基因突变, 儿科护理学

Abstract:

The primary objective of this study is to share the perioperative nursing experience of whole lung lavage for a pulmonary alveolar proteinosis（PAP）child with IRAS gene mutation. The key points of perioperative nursing measurements comprise evaluating children’ tolerance of lavage procedure,improving preoperative preparation and applying play therapy to alleviate children’s distress and oxygen uptake before the operation;enhancing the cooperation with doctors and monitoring the oxygen saturation during the operation;enhancing the airway care,preventing infections and monitoring complications after the operation. The symptoms of dyspnea were greatly improved and the blood oxygen saturation reached to expectations after twice of bronchoalveolar lavage.

Key words: Pulmonary Alveolar Proteinosis, Bronchoalveolar Lavage, Gene Mutation, Pediatric Nursing