1例单核细胞减少与分枝杆菌感染综合征伴肺泡蛋白沉积症患儿的护理

doi:10.3761/j.issn.0254-1769.2024.11.005

摘要/Abstract

摘要：

总结1例单核细胞减少与分枝杆菌感染综合征伴肺泡蛋白沉积症患儿行造血干细胞移植的护理经验。护理要点：成立多学科团队，完善入移植仓前准备；通过精细化护理控制感染，促进骨髓造血功能重建；密切监测病情变化，预防心肺功能衰竭；实施预见性护理，加强疾病管理；制订精准的服药方案，观察药物疗效及不良反应；开展叙事护理，缓解患儿负性情绪；制订个性化随访计划，实施优质的延续性护理。经过精心的治疗与护理，患儿顺利完成造血干细胞移植，移植后第41天，康复出院。随访1个月，恢复良好。

关键词: 免疫缺陷, 单核细胞减少与分枝杆菌感染综合征, 肺泡蛋白沉积症, 造血干细胞移植, 护理

Abstract:

To summarize the nursing experience of hematopoietic stem cell transplantation for a child with monocytopenia and mycobacterium infection syndrome complicated with pulmonary alveolar proteinosis. The key aspects of nursing encompass the establishment of a multidisciplinary diagnostic and treatment team，as well as the enhancement of warehousing preparation. Fine nursing plays a pivotal role in infection prevention and control，while also promoting hematopoietic reconstruction. Vigilant monitoring of condition changes is crucial to proactively prevent cardiopulmonary failure. Moreover，an intensified management approach towards underlying diseases should be implemented alongside predictive nursing interventions. The utilization of precision medication plans allows for the observation of drug efficacy and adverse reactions. Narrative nursing serves as a foundation to alleviate the child’s inner concerns，while personalized follow-up plans ensure the continuity of high-quality care. With careful treatment and care，the child successfully underwent hematopoietic stem cell transplantation. After 41 days post-transplantation，the child was discharged from the hospital after a successful recovery. The follow-up after a month showed good progress.

Key words: Immunodeficiency, Monocytopenia and Mycobacterium Infection Syndrome, Alveolar Proteinosis, Hematopoietic Stem Cell Transplantation, Nursing Care

周玮炜, 周钰珊, 潘政雯, 许丽炜, 章建丽, 金爱云, 周晓瑜. 1例单核细胞减少与分枝杆菌感染综合征伴肺泡蛋白沉积症患儿的护理[J]. 中华护理杂志, 2024, 59(11): 1319-1323.

ZHOU Weiwei, ZHOU Yushan, PAN Zhengwen, XU Liwei, ZHANG Jianli, JIN Aiyun, ZHOU Xiaoyu. Nursing care of a child with monocytopenia and mycobacterial infection syndrome and pulmonary alveolar proteinosis[J]. Chinese Journal of Nursing, 2024, 59(11): 1319-1323.

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