1例鸟氨酸氨甲酰基转移酶缺乏症患儿行肝移植的围手术期护理

doi:10.3761/j.issn.0254-1769.2022.13.013

摘要/Abstract

摘要：

总结1例鸟氨酸氨甲酰基转移酶缺乏症患儿行肝移植的围手术期护理经验。护理要点包括：高血氨急性期做好血液净化的护理;高血氨缓解期实施预见性护理;早期贯序抗凝治疗,做好出血的观察和护理;早期渐进性康复训练,促进患儿的生长发育;全程心理疏导,缓解患儿及其家长的负性情绪;提供个性化出院指导,进行延续性康复护理。经过20 d的治疗与护理,患儿康复出院,随访4个月,恢复良好。

关键词: 鸟氨酸氨甲酰基转移酶缺乏症, 高氨血症, 肝移植, 儿科护理学

Abstract:

To summarize the perioperative nursing experience of a child with ornithine transcarbamlase deficiency after liver transplantation. Key points of nursing care：blood purification care were taken in the acute stage of high blood ammonia;predictive care were adopted during the remission period of high blood ammonia;early sequential anticoagulation treatment was carried out and supplemented by bleeding observation and nursing;early progressive rehabilitation training were taken to promote the growth and development of the child;psychological counseling was applied through the whole process to relieve the negative emotions of the child and their parents;personalized discharge guidance and continuous rehabilitation care were provided. After 20 days of treatment and care,the child recovered and was discharged,followed up for 4 months and recovered well up to now.

Key words: Ornithine Transcarbamylase Deficiency, Hyperammonemia, Liver Transplantation, Pediatric Nursing

王芳, 卢芳燕. 1例鸟氨酸氨甲酰基转移酶缺乏症患儿行肝移植的围手术期护理[J]. 中华护理杂志, 2022, 57(13): 1618-1622.

WANG Fang, LU Fangyan. Perioperative nursing care of a child with otrnithine transcarbamlase deficiency undergoing liver transplantation[J]. Chinese Journal of Nursing, 2022, 57(13): 1618-1622.

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