7例囊性纤维化患儿的护理

doi:10.3761/j.issn.0254-1769.2022.18.013

摘要/Abstract

摘要：

总结7例囊性纤维化患儿的护理经验。护理要点：采集汗氯试验标本,协助诊断;促进气道廓清,改善患儿呼吸功能;加强电解质监测,及时纠正电解质紊乱;合理用药,缓解患儿症状;制订营养方案,改善患儿营养状况;加强出院宣教,提高患儿出院后生活质量。7例患儿经过积极治疗及精心护理均好转出院。

关键词: 囊性纤维化, 基因突变, 儿科护理学

Abstract:

The nursing care experience of 7 patients with cystic fibrosis is summarized in this article. The critical points of nursing care are recapitulated as followed：collecting the sweat chlorine test specimen to assist diagnosis;promoting airway secretion discharge to improve respiratory function;strengthening electrolyte monitoring to correct electrolyte disorder;promoting rational medicine use to alleviate patient symptoms;developing a nutritional plan to improve patient nutritional status;strengthening discharge education to improve patient quality of life. The result is desirable that symptoms of all patients were alleviated and they were discharged from our center after active treatment and diligent care.

Key words: Cystic Fibrosis, Gene Mutation, Pediatric Nursing

余红, 徐晓凤, 余卓文, 张玉蓉, 张晓蕾, 周壹文. 7例囊性纤维化患儿的护理[J]. 中华护理杂志, 2022, 57(18): 2256-2260.

YU Hong, XU Xiaofeng, YU Zhuowen, ZHANG Yurong, ZHANG Xiaolei, ZHOU Yiwen. Nursing care of 7 children with cystic fibrosis[J]. Chinese Journal of Nursing, 2022, 57(18): 2256-2260.

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