1例谷固醇血症患儿的护理

doi:10.3761/j.issn.0254-1769.2021.12.014

中华护理杂志 ›› 2021, Vol. 56 ›› Issue (12): 1843-1845.DOI: 10.3761/j.issn.0254-1769.2021.12.014

1例谷固醇血症患儿的护理

陈梅雪(), 宋元宗, 张妮, 林清然(), 陈伟菊

510632 广州市暨南大学护理学院（陈梅雪,张妮,林清然,陈伟菊）;暨南大学附属第一医院新生儿科（宋元宗）

收稿日期:2021-06-24 出版日期:2021-12-15 发布日期:2021-12-20
通讯作者: 林清然,E-mail： qingranlin@126.com
作者简介:陈梅雪：女,本科（硕士在读）,护师,E-mail： meixue789@163.com

Nursing care of a child with sitosterolemia

CHEN Meixue(), SONG Yuanzong, ZHANG Ni, LIN Qingran(), CHEN Weiju

Received:2021-06-24 Online:2021-12-15 Published:2021-12-20

摘要/Abstract

摘要：

总结1例8岁谷固醇血症患儿的护理经验。护理要点包括：制订个性化饮食清单,限制植物固醇和动物固醇摄入;监测患儿生长发育指标,评估其营养状况;观察并记录黄瘤变化情况,减少黄瘤带来的困扰;密切观察病情,预防并发症;加强心理护理,缓解患儿及其家属的消极情绪;定期随访,开展延续护理,提升患儿及其家属对疾病的管理能力。持续随访20个月,患儿症状改善,未发现相关并发症。

关键词: 谷固醇血症, 儿童, 饮食指导, 随访, 护理

Abstract:

This article aims to summarize the experience in the nursing care of an 8-year-old child with sitosterolemia. The mainly nursing points are as follows：to formulate a personalized diet list,to restrict the intake of plant sterols and some animal sterols;to monitor the growth and development indicators and assess nutritional status;to observe and record changes in xanthomas and reduce their disturbance;to closely observe the condition to prevent complications;to strengthen psychological care for the child and family members to relieve their negative emotions;to conduct regular follow-up and continued care to improve disease management capabilities of the child and his family. After 20 months of continuous follow-up,the patient’s condition improved without any complications.

Key words: Sitosterolemia, Child, Dietary Guidance, Follow-Up, Nursing Care

陈梅雪, 宋元宗, 张妮, 林清然, 陈伟菊. 1例谷固醇血症患儿的护理[J]. 中华护理杂志, 2021, 56(12): 1843-1845.

CHEN Meixue, SONG Yuanzong, ZHANG Ni, LIN Qingran, CHEN Weiju. Nursing care of a child with sitosterolemia[J]. Chinese Journal of Nursing, 2021, 56(12): 1843-1845.

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1例谷固醇血症患儿的护理

Nursing care of a child with sitosterolemia

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