1例先天性簇绒肠病患儿的营养管理

doi:10.3761/j.issn.0254-1769.2022.12.016

中华护理杂志 ›› 2022, Vol. 57 ›› Issue (12): 1512-1515.DOI: 10.3761/j.issn.0254-1769.2022.12.016

1例先天性簇绒肠病患儿的营养管理

陈晓飞(), 陈朔晖(), 李美, 沈倩倩, 范美花

310052 杭州市国家儿童健康与疾病临床医学研究中心/浙江大学医学院附属儿童医院消化内科（陈晓飞,李美,沈倩倩,范美花）,医院感染管理科（陈朔晖）

收稿日期:2021-11-03 出版日期:2022-06-20 发布日期:2022-06-13
通讯作者: 陈朔晖,E-mail： chcsh2@zju.edu.cn
作者简介:陈晓飞：女,硕士,副主任护师,护士长,E-mail： hzxiao0914@163.com
基金资助:
浙江省医药卫生科技计划面上项目(2020KY170)

Nutritional support management of a child with congenital tufting enteropathy

CHEN Xiaofei(), CHEN Shuohui(), LI Mei, SHEN Qianqian, FAN Meihua

Received:2021-11-03 Online:2022-06-20 Published:2022-06-13

摘要/Abstract

摘要：

先天性簇绒肠病属于罕见疾病,疾病早期患儿常因顽固性腹泻危及生命,营养管理是其护理难点。该文总结l例先天性簇绒肠病患儿营养管理经验。护理要点：开展营养筛查及评估,为制订个性化营养支持方案提供依据;尽早开展肠外营养支持,追赶体重增长,维持水、电解质平衡;及时给予肠内营养支持,改善患儿营养状况;预防并及时干预常见并发症。经过60 d积极治疗与精心护理,患儿病情得到控制,身高、体重稳步增长。

关键词: 先天性簇绒肠病, 营养不良, 营养支持, 儿科护理学

Abstract:

Congenital tufting enteropathy is rare to see in clinic,and it could be life-threatening due to intractable diarrhea in the early stage. The nutrition management was the most important and difficult part of nursing care. This study aimed to summarize the nutritional support experience of a case with congenital tufting enteropathy. In this case,we provide the personalized nutrition support based on nutrition screening and evaluation,and carry out parenteral nutrition support as soon as possible to help the child get fully potential of growth,as well as to get the metabolism balance. Besides,the timely enteral nutrition support was also used to improve the nutritional status of the child. Prevention and timely intervention for common complications were used to achieve clinical benefits. After a 60-day nursing care,the child’s condition was well-controlled with steady increasing in height and weight.

Key words: Congenital Tufting Enteropathy, Malnutrition, Nutritional Support, Pediatric Nursing

陈晓飞, 陈朔晖, 李美, 沈倩倩, 范美花. 1例先天性簇绒肠病患儿的营养管理[J]. 中华护理杂志, 2022, 57(12): 1512-1515.

CHEN Xiaofei, CHEN Shuohui, LI Mei, SHEN Qianqian, FAN Meihua. Nutritional support management of a child with congenital tufting enteropathy[J]. Chinese Journal of Nursing, 2022, 57(12): 1512-1515.

参考文献 18

[1]	Reifen RM, Cutz E, Griffiths AM, et al. Tufting enteropathy:a newly recognized clinicopathological entity associated with refractory diarrhea in infants[J]. J Pediatr Gastroenterol Nutr, 1994, 18(3):379-385. DOI URL
[2]	Goulet O, Salomon J, Ruemmele F, et al. Intestinal epithelial dysplasia(tufting enteropathy)[J]. Orphanet J Rare Dis, 2007, 20(2):20.
[3]	Tesouro Rodrí guez L, Lázaro de Lucas C, Magallares Garcí a LN, et al. Manejo y pronóstico de la displasia epitelial intestinal[J]. Anales De Pediatría, 2018, 88(1):48-49. DOI URL
[4]	钟燕. 儿童营养风险筛查[J]. 中华实用儿科临床杂志, 2016, 31(23):1765-1768.
	Zhong Y. Nutrition risk screening in children[J]. Chin J Appl Clin Pediatr, 2016, 31(23):1765-1768.
[5]	Hulst JM, Zwart H, Hop WC, et al. Dutch national survey to test the STRONG kids nutritional risk screening tool in hospitalized children[J]. Clin Nutr, 2010, 29(1):106-111. DOI URL
[6]	洪莉. 0-6月龄婴儿营养评估[J]. 中国实用儿科杂志, 2019, 34(10):818-822.
	Hong L. Nutritional assessment for 0-6 months old infants[J]. Chin J Pract Pediatr, 2019, 34(10):818-822.
[7]	WHO Multicentre Growth Reference Study Group. WHO Child Growth Standards based on length/height,weight and age[J]. Acta Paediatr Suppl, 2006, 450:76-85.
[8]	石汉平, 许红霞, 李苏宜, 等. 营养不良的五阶梯治疗[J]. 肿瘤代谢与营养电子杂志, 2015, 2(1):29-33.
	Shi HP, Xu HX, Li SY, et al. Five-step treatment for malnutrition[J]. Electron J Metab Nutr Cancer, 2015, 2(1):29-33.
[9]	Mihatsch WA, Braegger C, Bronsky J, et al. ESPGHAN/ESPEN/ESPR/CSPEN guidelines on pediatric parenteral nutrition[J]. Clin Nutr, 2018, 37(6 Pt B):2303-2305. DOI PMID
[10]	Sy J, Gourishankar A, Gordon WE, et al. Bicarbonate kinetics and predicted energy expenditure in critically ill children[J]. Am J Clin Nutr, 2008, 88(2):340-347. DOI URL
[11]	Olieman J, Kastelijn W. Nutritional feeding strategies in pediatric intestinal failure[J]. Nutrients, 2020, 12(1):177. DOI URL
[12]	孙红, 陈利芬, 郭彩霞, 等. 临床静脉导管维护操作专家共识[J]. 中华护理杂志, 2019, 54(9):1334-1342.
	Sun H, Chen LF, Guo CX, et al. Expert consensus on venous catheter maintenance[J]. Chin J Nurs, 2019, 54(9):1334-1342.
[13]	崔钰, 盖恬恬, 何月, 等. 危重症患者再喂养综合征识别及预防的研究进展[J]. 中华护理杂志, 2019, 54(9):1419-1422.
	Cui Y, Gai TT, He Y, et al. The prevention of refeeding syndrome:a review[J]. Chin J Nurs, 2019, 54(9):1419-1422.
[14]	龙兴霞, 姚梅琪, 姚金兰, 等. ICU肠内营养患者再喂养综合征发生现状及影响因素研究[J]. 中华护理杂志, 2021, 56(6):818-823.
	Long XX, Yao MQ, Yao JL, et al. Investigation and analysis of factors related to refeeding syndrome in ICU patients undergoing enteral nutrition[J]. Chin J Nurs, 2021, 56(6):818-823.
[15]	桂永浩, 薛辛东. 儿科学[M]. 3版. 北京: 人民卫生出版社, 2019, 72-75.
	Gui YH, Xue XD. Pediatrics[M]. 3rd edition. Beijing: People’s Medical Publishing House, 2019,72-75.
[16]	王金玲, 蔡威, 王莹. 小儿肠衰竭治疗策略研究进展[J]. 临床儿科杂志, 2021, 39(8):621-624.
	Wang JL, Cai W, Wang Y. Strategy of management in pediatric patients with intestinal failure[J]. J Clin Pediatr, 2021, 39(8):621-624.
[17]	陈前程, 范超, 易利纯. 跟踪随访在婴幼儿肠吸收不良综合征患儿中的应用效果[J]. 中国临床护理, 2020, 12(4):330-331,334.
	Chen QC, Fan C, Yi LC. The application effect of follow-up in infants with intestinal malabsorption syndrome[J]. Chin Clin Nurs, 2020, 12(4):330-331,334.
[18]	袁传杰, 黄倬, 孙小妹, 等. EPCAM基因突变所致先天性簇绒肠病1例报告并文献复习[J]. 临床儿科杂志, 2018, 36(8):618-620.
	Yuan CJ, Huang Z, Sun XM, et al. Congenital tufting enteropathy caused by mutation of EPCAM gene:a case report and review of literature[J]. J Clin Pediatr, 2018, 36(8):618-620.

1例先天性簇绒肠病患儿的营养管理

Nutritional support management of a child with congenital tufting enteropathy

RichHTML

PDF

可视化

摘要/Abstract

引用本文

使用本文

参考文献 18

相关文章 15

编辑推荐

Metrics

[1]	成磊, 钱佳艺, 段明霞, 黄海英, 王颖雯. 专业照护者感知的癌症患儿向成人过渡影响因素的质性研究[J]. 中华护理杂志, 2022, 57(9): 1048-1053.
[2]	刘美华, 彭剑雄, 罗翠, 郑焱, 朱丽辉, 肖政辉, 张新萍, 李庆博, 熊亮. 机械通气患儿早期活动方案的构建及应用研究[J]. 中华护理杂志, 2022, 57(8): 901-907.
[3]	孙丽, 胡成文, 刘群慧, 方敏, 顾道琴, 许宝惠. 1例急性白血病患儿的安宁疗护实践[J]. 中华护理杂志, 2022, 57(8): 992-995.
[4]	傅来建, 卢芳燕. 1例肝移植术后肺部卡氏肺孢子感染并发颅内出血患儿的护理[J]. 中华护理杂志, 2022, 57(8): 996-1000.
[5]	张娟, 何娇, 罗黎, 张岚, 韩燕红. 新生儿医用粘胶相关性皮肤损伤预防及管理的最佳证据总结[J]. 中华护理杂志, 2022, 57(8): 1008-1012.
[6]	赵丽华, 万兴丽, 朱友菊, 蒲倩婷, 胡艳玲, 史泽瑶, 刘玉兰, 陈晓娟, 付丽. NICU早产儿基于行为线索的经口喂养模式的研究进展[J]. 中华护理杂志, 2022, 57(8): 1013-1018.
[7]	黄勤, 张晓波, 顾莺, 胡静, 孔梅婧, 傅唯佳. 儿童静脉输液过程质量监控数据表的构建及应用[J]. 中华护理杂志, 2022, 57(7): 823-826.
[8]	余群飞, 张玉萍, 任英, 许国萍, 马姚静, 赵腾飞. 1例Ⅲ型戈谢病伴重度脊柱后凸畸形患儿的围手术期护理[J]. 中华护理杂志, 2022, 57(6): 736-739.
[9]	林楠, 诸纪华, 徐红贞, 周红琴. 早产儿体位管理的最佳证据总结[J]. 中华护理杂志, 2022, 57(4): 486-492.
[10]	吕璐洋, 王华芬, 卢芳燕, 王燕, 郑力. 住院患儿家庭出院准备度评估工具的研究进展[J]. 中华护理杂志, 2022, 57(4): 507-512.
[11]	慎斐, 罗飞翔, 商祯茹, 凌云. 吊床体位促进早产儿生长发育效果的研究[J]. 中华护理杂志, 2022, 57(3): 301-305.
[12]	谢帅华, 杨芹, 吴旭红, 蒋衍, 李烨文, 周佳, 李微, 黑明燕. 早产儿经口置入胃管置管长度测量方法的改良及效果评价[J]. 中华护理杂志, 2022, 57(2): 193-196.
[13]	卢露, 卢芳燕, 张婉莹, 姚彩萍. 1例肝豆状核变性并发肾功能衰竭患儿行肝移植术的护理[J]. 中华护理杂志, 2022, 57(2): 208-211.
[14]	林光燕, 熊俊, 魏平, 吴玉洁. 1例急性淋巴细胞白血病合并腹股沟坏死性筋膜炎患儿的护理[J]. 中华护理杂志, 2022, 57(2): 212-214.
[15]	张嘉欣, 郑乔木, 周菁鑫, 花文哲. 同伴支持在早产儿父母中的研究进展[J]. 中华护理杂志, 2022, 57(2): 245-250.